Myotonic Dystrophy

MYOTONIC DYSTROPHY
ENTER
GREET THE EXAMINERS
SANITISE YOUR HANDS
SHAKE HANDS WITH THE PATIENT AND THE GRIP RELEASE WILL BE SLOW
FACE
FRONTAL BALDING
TEMPORAL WASTING
PTOSIS
CATARACT
FACIAL MUSCLE WASTING
CHECK PUPILS AND CHECK CRANIAL NERVES 3,4,5,6,7
SHOULDER AND HANDS
SEE MUSCLE WASTING SPARING DELTOID
CHECK DISTAL MUSCLE WASTING
CHECK POWER IN PROXIMAL AND DISTAL MUSCLE GROUPS
CHECK RELEXES
PERCUSS THE THENAR EMINENCE TO DEMONSTRATE PERCUSSION MYOTONIA
ASK PATIENT TO MAKE A CLOSE FIST AND RELEASE
DO CHECK VIBRATION SENSATION DISTALLY ON LOWER LIMBS

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