Marfan's Syndrome

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EXAM IS CARRIED OUT FIRST BY SITTING THEN BY STANDING
SITTING

Enter

Greet the Examiner

Sanitize your hands

Introduce yourself to the examiner

Inspect around for any clues

YOU CAN FIND A TALL PATIENTS, NOT EVERYONE WHO ARE TALL HAS MARFAN SYNDROME,
SOME OF THEM HAS MARFANOID HABITUS

ARACHANODACTYLY, LOOK FOR THUMB SIGN, WRIST SIGN, PALPATE PULSE, CHECK
RADIORADIAL DELAY, OFFER BP AND CHECK FOR COLLAPSING PULSE AND ALSO ANY
PERIPHERAL STIGMATA OF IE

BLUE SCLERA, LOOK FOR IRIDODONESIS I.E THE VIBRATION OF THE IRIS WITH THE EYE MOVEMENT, THIS SHOULD RISE THE SUSPICION OF ECTOPIA LENTIS.

HIGH ARCHED PALATE AND CROWDED TEETH

LONG AND NARROW FACE

PECTUS EXCAVATUM, CARINATUM, DRAINAGE SCARS, PREVIOUS VATS SCAR (PNEUMOTHORAX), AUCULTATE LUNGS FOR PTX AND AUSCULTATE HEART FOR BOTH AR MURMUR AND MVP

STRIAE + OFFER TO ASSESS INGUINGAL HERNIA

NEURO ASSESMENT FOR WEAKNESS, SENSATIONA ND DURAL ECTASIA
STANDING HEIGHT ARM SPAN
PES PLANUS
KYPOSCOLIOSIS

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